|Title||Restoration of Global Sagittal Alignment After Surgical Correction of Cervical Hyperlordosis in a Patient with Emery-Dreifuss Muscular Dystrophy: A Case Report.|
|Publication Type||Journal Article|
|Year of Publication||2020|
|Authors||Diebo BG, Shah NV, Messina JC, Naziri Q, Post NH, K Riew D, Paulino CB|
|Journal||JBJS Case Connect|
|Date Published||2020 Jan-Mar|
|Keywords||Cervical Vertebrae, Female, Humans, Lordosis, Muscular Dystrophy, Emery-Dreifuss, Osteotomy, Spinal Fusion, Young Adult|
CASE: We report a rare cervical hyperlordotic deformity in a 19-year-old woman with Emery-Dreifuss muscular dystrophy and concomitant scoliosis. After standard posterolateral instrumentation and fusion of C2-T1 and extensive soft-tissue release, her neck pain improved and unassisted maintenance of cervical alignment and horizontal gaze were preserved through an 8-year follow-up. More importantly, she exhibited reciprocal correction of compensatory global sagittal malalignment, including lumbar lordosis.
CONCLUSIONS: This case highlights the importance of full-spine analysis for all patients with spinal deformity to identify and differentiate primary driver(s) of deformity from compensatory mechanisms to individualize treatment toward what truly drives the patient's disability.
|Alternate Journal||JBJS Case Connect|