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Restoration of Global Sagittal Alignment After Surgical Correction of Cervical Hyperlordosis in a Patient with Emery-Dreifuss Muscular Dystrophy: A Case Report.

TitleRestoration of Global Sagittal Alignment After Surgical Correction of Cervical Hyperlordosis in a Patient with Emery-Dreifuss Muscular Dystrophy: A Case Report.
Publication TypeJournal Article
Year of Publication2020
AuthorsDiebo BG, Shah NV, Messina JC, Naziri Q, Post NH, K Riew D, Paulino CB
JournalJBJS Case Connect
Volume10
Issue1
Paginatione0003
Date Published2020 Jan-Mar
ISSN2160-3251
KeywordsCervical Vertebrae, Female, Humans, Lordosis, Muscular Dystrophy, Emery-Dreifuss, Osteotomy, Spinal Fusion, Young Adult
Abstract

CASE: We report a rare cervical hyperlordotic deformity in a 19-year-old woman with Emery-Dreifuss muscular dystrophy and concomitant scoliosis. After standard posterolateral instrumentation and fusion of C2-T1 and extensive soft-tissue release, her neck pain improved and unassisted maintenance of cervical alignment and horizontal gaze were preserved through an 8-year follow-up. More importantly, she exhibited reciprocal correction of compensatory global sagittal malalignment, including lumbar lordosis.

CONCLUSIONS: This case highlights the importance of full-spine analysis for all patients with spinal deformity to identify and differentiate primary driver(s) of deformity from compensatory mechanisms to individualize treatment toward what truly drives the patient's disability.

DOI10.2106/JBJS.CC.19.00003
Alternate JournalJBJS Case Connect
PubMed ID31899720